1. Biology Dictionary
  2. Carnitine palmitoyltransferase1 (CPT1)

Carnitine palmitoyltransferase1 (CPT1)肉碱棕榈酰转移酶 1

释义:

Carnitine palmitoyltransferase1is the key enzyme in the carnitine-dependent transport across the mitochondrial inner membrane and its deficiency results in a decreased rate of fatty acid beta-oxidation. Carnitine palmitoyltransferase1shows 3 isoform including liver, brain, and muscle isoforms.

肉碱棕榈酰转移酶 1 (CPT1) 是肉碱依赖性跨线粒体内膜转运的关键酶,其缺乏导致脂肪酸-氧化率降低。肉碱棕榈酰转移酶1有肝脏型、脑型和肌肉型3种亚型。

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